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Pathways of ammonia detoxification to GLN in muscles linked to Improved intake of your BCAA and α-KG (cataplerosis) and suggested effects of BCAA and phenylbutyrate in subjects with liver cirrhosis or UCD. Good impact of BCAA on ammonia detoxification to GLN could possibly be blunted by GLN degradation to ammonia in enterocytes and kidneys. Phenyl